Idiopathic inflammatory myopathies: epidemiology, classification, and diagnostic criteria

  • Frank L Mastaglia
    Correspondence
    Corresponding author. Centre for Neuromuscular and Neurological Disorders, 4th floor, A Block, QEII Medical Centre, Nedlands, Western Australia, Australia
    Affiliations
    Centre for Neuromuscular and Neurological Disorders, QEII Medical Centre, Nedlands, Western Australia, Australia

    Department of Medicine, University of Western Australia, Australia

    Department of Neurology and Clinical Neurophysiology, Sir Charles Gairdner Hospital, Nedlands, Australia
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  • Beverley A Phillips
    Affiliations
    School of Physiotherapy, University of Melbourne, Carlton, Victoria, Australia
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      The idiopathic inflammatory myopathies (IIMs) are a heterogeneous group of immune-mediated disorders, that may present in an isolated form, or in association with another autoimmune or connective tissue disease, a malignancy, or, rarely, an infection or other environmental exposure. This article summarizes recent findings on epidemiologic aspects of the three major varieties of IIM (dermatomyositis, polymyositis and inclusion body myositis) and proposes schemes for the classification and diagnostic criteria for these conditions.
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